معرفی یک بیمار مبتلا به هیستیوسیتوزیس ایکس از نوع hand schuller christian disease

معرفی یک بیمار مبتلا به هیستیوسیتوزیس ایکس از نوع Hand Schuller Christian disease

The term histiocytosis refers to a group of idiopathic clinics entities characterized by diffuse proliferation of mature histiocytes associated with tumorlike masses of foamy reticuloendothelial cells containing lipoid droplets with variable number of eosinophiles and connective tissue. This cells causes tumorlike masses in the bones and other vicera in the body thus it may have very different ...

Hand--schuller--christian Disease.

ENDOCRINOLOGICAL, METABOLIC DISORDERS hypophysis dysfunction diabetes insipidus GENITAL DISORDERS genital dysfunctions puberty, delayed HEMOPOIETIC-LYMPHORETICULAR SYSTEM DISORDERS lymphonodus disorders lymphonodus enlarged, lymphadenopathy spleen, anomalies splenomegaly, hepatosplenomegaly LABORATORY DATA lymphoreticular system, changes histiocytosis, including histiocytoma myelo-erythropoieti...

[Hand-Schuller-Christian disease (report of a case)].

One Case-report of Hand-Schuller-christian Syndrome in Children

SUMMARY Histiocytosis X is associated with idiopathic Proliferation of histiocytes and infiltration of eosinophils in bone marrow Spleen, Liver and other Soft tissues. Clinically there are three distinct forms:  1 - Eosinophilic granuloma is the most benign and Localized form of the disease.  2- Letterer- Siwe is the most malignant, generalized and fatal form of the disease.  3- Hand- Schul...

Hand schuller christian disease: a rare case report with oral manifestation.

Langerhan's Cell Histiocytosis (LCH) is disorders which include abnormalities that result from abnormal proliferation of langerhan's cells or their precursors. LCH is clinically classified into three types-eosinophilic granuloma, Hand Schuller Christian disease and Abt-Letterer- Siwe disease. It is usually manifested in childhood as well as in adulthood. The clinical manifestations are the resu...

Dexmedetomidine: A Saviour in a Child with Hand Schuller Christian Disease for MRI

Hand Schuller Christian disease (HSC) primarily affects infants and children. Its classical presentation includes triad of exophthalmos, diabetes insipid us, and calvariallytic lesions. Systemic involvement may include hepatomegaly, lymphadenopathy, dermatological, gastrointestinal tract, renal, pulmonary and CNS involvement. CNS involvement includes convulsions, increased intracranial pressure...